Facomatose Pigmentovascular: Relato de Caso
Phacomatosis pigmentovascularis: Case report
Facomatose Pigmentovascular: Relato de Caso
Thayla Baptista Campostrini; Renata Souza Lorenzoni; Priscila Tavares Andrade Dutra; Helena Arantes Pelegrine; Hannah Cade Guimarães; Christine Chambô Pignaton
Resid Pediatr. 2019;9(3):330-332 - Relato de Caso - DOI: 10.25060/residpediatr-2019.v9n3-28
Phacomatosis pigmentovascularis is defined as the association of a vascular malformation with an extensive pigment nevus. It is currently classified by Happle into three groups: cesioflamea, spilorosea and cesiomarmorata. We report a case of a female newborn presenting with typical manifestations of cesioflamea phacomatosis pigmentovascularis, according to the classification above. The rarity of this genodermatosis, the clinical exuberance of the skin lesions and the need for recognition of this syndrome and its repercussions motivated this case report.